Pseudohupoaldosteronsm and apparent mineralocorticoid excess
Two faces, two pediatric patients
DOI:
https://doi.org/10.51987/Rev.Hosp.Ital.B.Aires.v36i1.688Keywords:
apparent mineralocorticoid excess, aldosterone, type 2 11 β hidroxiesteroide deshidrogenase, PseudohypoaldosteronismAbstract
Endocrinological syndromes with underactive or overactive hormonal levels with paradoxical dosages have been well characterized over the years of the twentieth century, from the development of genetic and molecular techniques. We present two patients with pseudohypoaldosteronism and apparent mineralocorticoid excess as mirror syndromes, with the aim to alert the clinician regarding their consideration as a diagnostic entity in children with fluid and electrolyte disturbances
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